Budd-Chiari Syndrome (Occlusion of the Hepatic Veins): Seven Cases

Article1 August 1954BUDD-CHIARI SYNDROME (OCCLUSION OF THE HEPATIC VEINS): SEVEN CASESEDDY D. PALMEREDDY D. PALMERSearch for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-41-2-261 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptThe Budd-Chiari syndrome, or Chiari's syndrome, is the disease complex which follows hepatic vein occlusion. It is a moderately well popularized secondary abdominal response to several disease processes, but the number of reported cases remains remarkably small. During the past 32 months seven autopsy-proved cases and four presumptive cases have been observed. This appears to be a large experience with the syndrome, perhaps explained by the fact that a large tumor center was the source of material. From 1910 to 1939 at the Mayo Clinic 20 instances were encountered.1 Only five were found during 11,979 autopsies at Stanford University.2Lambron...Bibliography Additional Useful References1. KelseyComfort MPMW: Occlusion of the hepatic veins: review of twenty cases, Arch. Int. Med. 75: 175-183, 1945. CrossrefGoogle Scholar2. ArmstrongCarnes CDWH: Obstruction of the hepatic veins (Chiari's disease): report of five cases, Am. J. M. Sc. 208: 470-478, 1944. CrossrefGoogle Scholar3. Budd G: Diseases of the liver, 1846, Lea & Blanchard, Philadelphia, p. 151. Google Scholar4. Chiari H: Über die selbständige Phlebitis obliterans der Hauptstämme der Venae hepaticae als Todesursache, Beitr. z. path. Anat. u. z. allg. Path. 26: 1-17, 1899. Google Scholar5. Hoover CF: Obstruction of hepatic veins, J. A. M. A. 74: 1753-1756, 1920. CrossrefGoogle Scholar6. KahnSpring SM: Thrombosis of the hepatic veins—Chiari's syndrome: report of a case with biopsy and venous pressure determination, Ann. Int. Med. 14: 1075-1083, 1940. LinkGoogle Scholar7. HirshManchester HLB: Chiari's syndrome: report of a case, New England J. Med. 235: 507-511, 1946. CrossrefMedlineGoogle Scholar8. Thompson RB: Thrombosis of the hepatic veins; the Budd-Chiari syndrome, Arch. Int. Med. 80: 602-615, 1947. CrossrefGoogle Scholar9. LittleMontgomery RDPO: Case report of stenosis of the vena cava with vena caval and hepatic vein thrombosis related to trauma, Ann. Int. Med. 37: 197-203, 1952. LinkGoogle Scholar10. Gee SJ: Complete obliteration of the mouths of the hepatic veins, St. Barth. Hosp. Rep. London 7: 144-146, 1871. Google Scholar11. HutchisonSimpson RSL: Occlusion of the hepatic veins with cirrhosis of the liver, Arch. Dis. Childhood 5: 167-186, 1930. CrossrefMedlineGoogle Scholar12. Hess AF: Fatal obliterating endophlebitis of hepatic veins, Am. J. M. Sc. 130: 986-1001, 1905. CrossrefGoogle Scholar13. ThompsonTurnbull THM: Primary occlusion of the ostia of the hepatic veins, Quart. J. Med. 5: 277-296, 1912. Google Scholar14. Nishikawa Y: Über die Obliteration der Stammlebervenen und des heparen Hohlvenenabschnittes (Thrombophlebitis obliterans venae hepaticae et venae cavae inferioris), Mitt. a. d. med. Fakult. d. k. Univ. zu Tokyo 20: 151-305, 1918-19. Google Scholar15. de Almeida AD: Contribuição para o estudo da anastomose espleno-renal (com especial atenção à via de acesso), Tese, Univ. de São Paulo, p. 243, 1951. Google Scholar16. Sohval AR: Hepatic complications in polycythemia vera, with particular reference to thrombosis of the hepatic and portal veins and hepatic cirrhosis, Arch. Int. Med. 62: 925-945, 1938. CrossrefGoogle Scholar17. Moore FC: Primary obliterative inflammation of main trunks of hepatic veins, M. Chron. 3: 240-251, 1902. Google Scholar18. Rosenblatt OG: Über einen Fall von abnormen Verlauf der Lebervenen in Verbindung mit Cirrhose und Carcinom der Leber und consecutiver carcinomatöser Infiltration des Peritoneums, Jahresb. u. d. Leistung. d. ges. Med. 1: 226-227, 1867. Google Scholar19. East T: Chiari's disease, with hypertrophic osteoarthropathy and familial lipomatosis, Proc. Roy. Soc. Med. 26: 272, 1932. CrossrefGoogle Scholar20. Kretz R: Pathologie der Leber, Ergebn. d. allg. Path. u. path. Anat. 82: 473-537, 1902. Google Scholar21. AltschuleWhite MDG: Chiari's syndrome in patient with polycythemia vera: report of case, New England J. Med. 220: 1030-1033, 1939. CrossrefGoogle Scholar22. Berk L: Ueber Thrombose der Lebervenen nach umscriebener Thrombose im hepatischen Stück der unteren Hohlvene, Beitr. z. path. Anat. u. z. allg. Path. 90: 509-512, 1932. Google Scholar23. Cole NB: Comments on case of polycythemia rubra vera with autopsy, M. Clin. North America 16: 1255-1265, 1933. Google Scholar24. Lüdeke H: Thrombophilie und Polycythemie, Virchows Arch. f. path. Anat. 293: 218-252, 1934. CrossrefGoogle Scholar25. McAlpinSmith KRKE: Polycythemia vera: report of fourteen cases treated with acetylphenylhydrazine, New York State J. Med. 38: 101-109, 1938. Google Scholar26. NormanAllen ILEV: The vascular complications of polycythemia, Am. Heart J. 13: 257-274, 1937. CrossrefGoogle Scholar27. Oppenheimer BS: Vascular occlusion in polycythemia vera, Tr. A. Am. Physicians 44: 338-344, 1929. Google Scholar28. Churton T: Case of cirrhosis of liver, apparently due to congenital syphilis, with thrombosis of hepatic veins, Tr. Path. Soc. London 50: 145, 1899. Google Scholar29. CoroniniOberson CG: Neue histologische Ergebnisse bei Endophlebitis obliterans hepatica, Virchows Arch. f. path. Anat. 298: 251-297, 1936. CrossrefGoogle Scholar30. JacobsonGoodpasture VCEW: Occlusion of entire inferior vena cava by hypernephroma, with thrombosis of hepatic vein and its branches, Arch. Int. Med. 22: 86-95, 1918. CrossrefGoogle Scholar31. BaehrKlemperer GP: Thrombosis of portal and of hepatic veins, M. Clin. North America 14: 391-410, 1930. Google Scholar32. Cabot Case no. 27431, New England J. Med. 225: 661-663, 1941. CrossrefGoogle Scholar33. CattanCarassoFrumusanLumbrosoSee RRPPP: Deux cas de syndrome de Budd-Chiari, Bull. et mém. Soc. méd. d. hôp. de Paris 69: 435-439, 1953. MedlineGoogle Scholar34. Detrie P: La thrombose des veines sus-hépatique (syndrome de Budd-Chiari), Presse méd. 60: 392-393, 1952. MedlineGoogle Scholar35. FruhlingRogerJobard LSP: Le syndrome hépatique de Chiari (occlusion des veines sus-hépatiques), Ann. méd. 52: 696-733, 1951. Google Scholar36. HallockWatsonBerman PCJL: Primary tumor of inferior vena cava, with clinical features suggestive of Chiari's disease, Arch. Int. Med. 66: 50-61, 1940. CrossrefGoogle Scholar37. Koshy P: Chiari's syndrome, Indian M. Gaz. 86: 556-558, 1951. MedlineGoogle Scholar38. SimondsCallaway JPJW: Anatomical changes in livers of dogs following mechanical constriction of hepatic veins, Am. J. Path. 8: 159-166, 1932. MedlineGoogle Scholar This content is PDF only. To continue reading please click on the PDF icon. Author, Article, and Disclosure InformationAffiliations: MC Washington, D. C.*Received for publication March 3, 1954.From the Gastroenterology Service, Walter Reed Army Hospital, Washington, D. C. 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