Highlights a rare variant of left ventricular non-compaction involving the interventricular septum and causing multiple ventricular septal defects, diagnosed via multimodality imaging.
Hypothesis-generating for septal-predominant LVNC with multiple VSDs in children; larger cohorts needed to assess prevalence and outcomes.
Left ventricular non-compaction (LVNC) is a congenital cardiomyopathy characterized by deep ventricular trabeculations thought to be due to an arrest of myocardial morphogenesis. Integration of various cardiac imaging modalities such as echocardiography, cardiac computed tomography and cardiac magnetic resonance imaging help in the diagnosis of this rare clinical entity. We describe a child with rare variant of LVNC with predominant involvement of interventricular septum resulting in multiple ventricular septal defects.
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Goel et al. (2015) studied this question.
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