Population
A family with true congenital idiopathic hypoprothrombinemia
Design
Case_series
Authors
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Alerts clinicians to differentiate true vs pseudo congenital hypoprothrombinemia; leaves open mechanistic characterization of thromboplastin formation.
Highlights the need to distinguish true congenital idiopathic hypoprothrombinemia from pseudo-hypoprothrombinemia caused by prothrombin conversion factor deficiencies.
S. Van Creveld (1954) studied this question.