This case report describes a rare presentation of Carney's triad in a patient with gastric leiomyosarcoma and pulmonary hamartomas, highlighting the need for careful monitoring for paraganglioma.
May warrant paraganglioma surveillance in similar patients; hypothesis-generating for Carney triad associations in Japan.
症例は, 32歳, 女性, 多発性でかつ増大傾向を示していた胸部腫瘤影を指摘されて紹介入院となった.右上葉切除を施行し, 軟骨性成分が主体の多発性肺過誤腫と診断された.この症例は, 13歳の時に胃平滑筋肉腫にて胃全摘術を施行された既往歴があったことから, Carney's triad (gastric epitheloidleiomyosarcoma, pulmonary chondroma, functioning extra-adrenal paraganglioma) の2項目を満たし, 極めて稀なCamay's syndrome の1例 (本邦2例目) と考えられた.今後, paraganglioma の発生に関して厳重な経過観察が必要と思われる.
No takes yet. Share an insight, caveat, or question.
Kawamura et al. (1994) studied this question.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: