Sickle Cell Trait and Superior Longitudinal Sinus Thrombosis

Case Studies1 March 1964Sickle Cell Trait and Superior Longitudinal Sinus ThrombosisERIC A. SCHENK, M.D.ERIC A. SCHENK, M.D.Author, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-60-3-465 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptRecognition of the varied clinical manifestations of sickle cell hemoglobin and its disorders has been repeatedly emphasized in the medical literature. The sickle cell disorders are the result of the inheritance of a dominant gene which determines the presence of abnormal hemoglobin S. In the homozygous individual (hemoglobin S-S) usually over 90 per cent of red cell hemoglobin will be hemoglobin S, and the disease is manifest as sickle cell anemia. If the genetic constitution is heterozygous (hemoglobin S-A), hemoglobin S will constitute up to 50 per cent of red cell hemoglobin, the remainder being normal adult hemoglobin A (and...References1. 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Author, Article, and Disclosure InformationAffiliations: Rochester, New YorkFrom the Department of Pathology, The University of Rochester School of Medicine and Dentistry and Strong Memorial Hospital, Rochester, New York.Dr. Schenk is an advanced fellow of the American Heart Association.Requests for reprints should be addressed to Eric A. Schenk, M.D., Department of Pathology, The University of Rochester School of Medicine and Dentistry and Strong Memorial Hospital, 260 Crittenden Boulevard, Rochester 20, New York. 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SWANSON, M.D.Thrombosis of the superior longitudinal sinusduring infancyBenign Intracranial Hypertension (Pseudotumor Cerebri)Aseptic necrosis of the femoral heads in sickle-A hemoglobin diseaseThe Management of Anæsthesia in Sickle Cell States [Abridged] 1 March 1964Volume 60, Issue 3Page: 465-470KeywordsAnemiaDentistryGeneticsHeartHemoglobinHospital medicineSickle cell diseaseSickle cell hemoglobinThrombosis Issue Published: 1 March 1964 PDF downloadLoading ...