Key result
Hirayama disease in mainland China presents as a benign self-limited disorder with juvenile preponderance and asymmetric muscular atrophy, showing no geographic difference in clinical presentation.
Population
192 patients (167 males, 25 females) with Hirayama disease from mainland China, mean age at onset 16.8 years.
Design
Case_series
Authors
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May reduce misdiagnosis as ALS in young Chinese patients; leaves open larger studies to confirm uniformity.
Observational (n=192)
Hirayama disease is a benign self-limited disorder with juvenile preponderance and asymmetric muscular atrophy of the distal upper limb, which is under-recognized in mainland China.
Zhou et al. (2010) conducted an observational in Hirayama disease (n=192). Hirayama disease vs. Patients from other countries or regions was evaluated on Clinical features and disease course. Hirayama disease in mainland China presents as a benign self-limited disorder with juvenile preponderance and asymmetric muscular atrophy, showing no geographic difference in clinical presentation.
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