Bullous Variety of Incontinentia Pigmenti (Bloch-Sulzberger)

INCONTINENTIA pigmenti is a rare congenital anomaly. It was first fully described under this name by Sulzberger1in 1927, and by Siemens2in 1929 as ``melanosis corii degenerativa.'' Sulzberger's case had been previously presented by Bloch3in 1925, and Siemens' case was discussed first in a dissertation by Lechleuthner.4According to Becker,5the condition was evidently described first by Bardach6as a systematized nevus. Carney7recently reviewed 32 cases from the literature (including the one reported in this paper) and added 5 more of his own. Additional cases are reported by heilesen8(two cases), Jaramillo and his associates,9Doornink10(three cases), and Uebel and his co-workers11; the last authors cited two additional observations (Hora, Gerard). This would bring the total to about 46 cases of incontinentia pigmenti. Actually the number of cases presented is greater, because