Role of Transesophageal Echocardiography in Patient with Tetralogy of Fallot with Unilateral Absence of Pulmonary Artery undergoing Intracardiac Repair

Unilateral absence of pulmonary artery (UAPA) is a rare congenital anomaly commonly associated with cardiovascular malformation. Tetralogy of Fallot (TOF) is the most frequent concomitant disorder for UAPA disease. Incidence of UAPA in TOF is 1 to 3%. The absent left pulmonary artery (LPA) is 5 to 8 times more frequent than the right pulmonary artery (RPA). In this case report, emphasis has been given to the role of transesophageal echocardiography (TEE) in patients with UAPA with TOF undergoing intracardiac repair.