Key result
Venoarterial extracorporeal membrane oxygenation followed by surgical repair successfully managed a rare case of a neonate with a large unrestrictive Gerbode defect and cardiogenic shock.
Why the study?
Congenital Gerbode defects are rarely hemodynamically significant, and neonatal cases resulting in cardiogenic shock are exceedingly rare.
Case Report (n=1)
A rare case of neonatal congenital Gerbode defect resulting in cardiogenic shock was successfully managed with VA-ECMO and surgical repair.
Large unrestrictive Gerbode defects can precipitate neonatal cardiogenic shock; this case leaves open optimal ECMO-to-repair strategies.
Congenital Gerbode defects, consisting of a deficiency in the membranous septum causing left ventricle-to-right atrium shunting, are rarely hemodynamically significant. Here, we present the case of a neonate with a large unrestrictive Gerbode defect, patent foramen ovale, patent ductus arteriosus, and pulmonary valve insufficiency resulting in a circular intracardiac shunt and cardiogenic shock. The patient was managed with venoarterial extracorporeal membrane oxygenation followed by neonatal Gerbode defect repair. After repair, the patient had an uncomplicated postoperative course. To our knowledge, a neonatal congenital Gerbode defect resulting in cardiogenic shock is exceedingly rare.
No takes yet. Share an insight, caveat, or question.
Kang et al. (2023) conducted a case report in Congenital Gerbode defect resulting in cardiogenic shock (n=1). Venoarterial extracorporeal membrane oxygenation followed by neonatal Gerbode defect repair was evaluated on Postoperative course. Venoarterial extracorporeal membrane oxygenation followed by surgical repair successfully managed a rare case of a neonate with a large unrestrictive Gerbode defect and cardiogenic shock.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: