Primary splenic angiosarcoma is a rare malignancy with a dismal prognosis that can present with rapid progression and fatal hemorrhage.
Alerts clinicians to rapid fatal hemorrhage in splenic angiosarcoma; leaves open optimal management strategies.
Primary angiosarcoma of the spleen is an extremely rare malignancy. Splenic angiosarcoma is difficult to diagnose, and treatment is often challenging. The prognosis is dismal, with a mean survival of less than 1 year. Currently, no standard treatment methods have been established. Anecdotal reports suggest that early diagnosis and prompt splenectomy followed by cytotoxic chemotherapy can be effective treatment modalities. We report a case of rapidly progressing primary splenic angiosarcoma with multiple liver and bone metastases and a fatal hemorrhagic outcome.
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Cho et al. (2013) studied this question.
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