This case report describes the rare occurrence and successful valve-sparing surgical excision of a papillary fibroelastoma on the pulmonary valve.
May support valve-sparing excision for rare pulmonary valve fibroelastoma; leaves open optimal strategies pending larger series.
Among primary cardiac tumors (prevalence 0.0017-0.28%), cardiac papillary fibroelastoma (CPF) is uncommon, 8% of cases, but it's the most frequent cardiac neoplasm originating from the endocardium. It usually involves left-sided heart valves, very rarely the pulmonary valve. Echocardiographically this neoplasm is a small mass, <20mm, almost 50% with a small stalk, and mobile. Macroscopically it appears similar to a "sea anemone". Clinically, CPF could be associated with coronary, cerebral, pulmonary and retinal emboli. We present the case of a 54year old man who came to our attention for the incidental discover at echocardiogram of a mobile mass attached to the ventricular side of the pulmonary valve. The patient underwent prompt surgical removal of the neoplasm through median sternotomy with sparing of the valve.
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Luca Caprili (2014) studied this question.
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