Key result
A 53-year-old male with an advanced intra-abdominal desmoplastic small round cell tumor underwent cytoreductive surgery and died months later.
Case Report (n=1)
No
This case report describes a rare presentation of intra-abdominal desmoplastic small round cell tumor in a 53-year-old patient who underwent cytoreductive surgery but died months later.
Poor survival after cytoreductive surgery in advanced disease warrants cautious selection; leaves open optimal strategies for this rare tumor.
The desmoplastic small round cell tumor (DSRCT) is a neoplasm of rare occurrence, described in 1987 by Sesterhennet al. Currently, there are about 101 cases described in the consulted literature. The authors report a case of intra-abdominal DSRCT in a 53-year-old patient, carrier of a palpable mass in epigastrium, asymptomatic. The propaedeutics showed multiple expansive lesions of varying dimensions compromising the peritoneal cavity. The patient was referred to exploratory laparotomy; only cytoreductive surgery was possible. The intraoperative findings are described, tomographic, and macroscopic and immunohistochemical aspects. The patient was followed up at the Oncology Service. He died months after surgery.
No takes yet. Share an insight, caveat, or question.
Drumond et al. (2014) conducted a case report in Desmoplastic small round cell tumor (n=1). Cytoreductive surgery was evaluated on Survival. A 53-year-old male with an advanced intra-abdominal desmoplastic small round cell tumor underwent cytoreductive surgery and died months later.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: