Population
Patients with idiopathic hyperlipemia (an inborn error of lipid metabolism)
Design
Review
Authors
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Alerts clinicians to ischemic heart disease risk in idiopathic hyperlipemia; leaves open prospective validation in contemporary cohorts.
Idiopathic hyperlipemia is an inborn error of lipid metabolism characterized by elevated serum lipids, xanthomas, and pancreatitis, and is no longer considered a benign condition, likely due to its association with ischemic heart disease.
David Brown (1961) studied this question.
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