Key result
The Bentall-De Bono procedure was successfully performed in a 35-year-old woman with Marfan syndrome and chronic Stanford type A aortic dissection, resulting in clinical improvement and hospital discharge.
Why the study?
Cardiovascular complications, particularly aortic dissection, are the leading cause of mortality in Marfan syndrome.
Case Report (n=1)
No
The Bentall-De Bono procedure remains an effective and safe surgical approach for managing chronic Stanford type A aortic dissection in patients with Marfan syndrome.
Supports feasibility of Bentall repair in symptomatic Marfan chronic type A dissection; leaves open optimal timing and selection criteria.
Marfan syndrome is a connective tissue disorder with multisystemic involvement, in which cardiovascular complications, particularly aortic dissection, are the leading cause of mortality. We report a case of a 35-year-old woman with known Marfan syndrome who complained of chest pain in the last 4 months and was found to have a chronic Stanford type A aortic dissection and severe aortic insufficiency. Surgical repair with a Bentall-De Bono procedure was successfully performed. This case highlights the importance of early recognition of chronic dissection in Marfan patients and the effectiveness of surgical management using the current gold standard approach.
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Ramírez-López et al. (2025) conducted a case report in Stanford Type A Chronic Aortic Dissection (n=1). Bentall-De Bono procedure was evaluated on Clinical improvement and hospital discharge. The Bentall-De Bono procedure was successfully performed in a 35-year-old woman with Marfan syndrome and chronic Stanford type A aortic dissection, resulting in clinical improvement and hospital discharge.
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