Neurological Syndromes Associated With Cervical and Craniocervical Anomalies

CONGENITAL abnormalities of the cervical region have long been recognized, the first report being that of Rokitansky in 1846. 1 Since then, there have been many accounts, but they have mainly described the anatomical defects. Only a few clinical reports have been published in detail since Homen 2 established a correlation between malformations in this region and neurological syndromes. Spillane et al 3 published their review, and further cases were reported by Bharucha and Dastur. 4 Both these reports deal mainly with the radiological or associated pathological features of the disease and relate them secondarily to the clinical features. Garcin and Oeconomos 5 reviewed 114 patients reported in the literature and added 18 of their own. They presented a complete clinical and radiological study, but, unfortunately, this review is not readily available to the practicing physician. We report 13 patients with bony abnormalities of the cervical region accompanied by