Key result
A 34-year-old female with unoperated double inlet left ventricle successfully survived into her fourth decade and presented with supraventricular tachycardia that reverted to sinus rhythm with adenosine.
Why the study?
Patients with double inlet left ventricle rarely survive beyond teenage years without surgical correction, and coexisting supraventricular tachycardia is rare and complicates diagnosis and management.
Case Report (n=1)
This case highlights the exceptional survival of a patient with uncorrected double inlet left ventricle into her fourth decade, whose condition was unmasked by an episode of supraventricular tachycardia.
Double inlet left ventricle (DILV) is a rare complex congenital heart defect characterized by the presence of two atrioventricular valve orifices leading into a single left ventricle. Patients rarely survive beyond teenage years without surgical correction. Supraventricular tachycardia (SVT) in DILV is a rare occurrence that adds an additional layer of complexity to diagnosis and management. Here, we report an exceptional case of DILV who survived well into her fourth decade of life without any surgical correction. The patient presented to us with SVT which lead to the discovery of her unique cardiac anomaly.
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Imamuddin et al. (2023) conducted a case report in Double inlet left ventricle (DILV) with supraventricular tachycardia (SVT) (n=1). Adenosine was evaluated on Reversion to sinus rhythm. A 34-year-old female with unoperated double inlet left ventricle successfully survived into her fourth decade and presented with supraventricular tachycardia that reverted to sinus rhythm with adenosine.
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