Key result
A 19-year-old female presenting with severe pulmonary artery hypertension in the early post-partum period was diagnosed with pulmonary capillary haemangiomatosis by open lung biopsy.
Why the study?
Pulmonary capillary haemangiomatosis is a rare cause of pulmonary hypertension that is often misdiagnosed as primary pulmonary hypertension and pulmonary veno-occlusive disease.
Case Report (n=1)
Answers are grounded in this paper and cite their sources.
Highlights pulmonary capillary haemangiomatosis as a rare cause of severe pulmonary hypertension that can be diagnosed via open lung biopsy.
Pulmonary capillary haemangiomatosis (PCH) is a rare disorder of unknown aetiology, characterised by proliferating capillaries that invade the pulmonary interstitium, alveolar septae and the pulmonary vasculature. It is often mis-diagnosed as primary pulmonary hypertension and pulmonary veno-occlusive disease. Pulmonary capillary haemangiomatosis is a locally aggressive benign vascular neoplasm of the lung. We report the case of a 19-year-old female who was referred to us in the early post-partum period with severe pulmonary artery hypertension, which was diagnosed as PCH by open lung biopsy. [
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Singh et al. (2022) conducted a case report in Pulmonary capillary haemangiomatosis (n=1). A 19-year-old female presenting with severe pulmonary artery hypertension in the early post-partum period was diagnosed with pulmonary capillary haemangiomatosis by open lung biopsy.
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