Key result
Among 892 patients with chronic heart block, 6 (0.67%) had neuromuscular disease related to the conduction disturbance, including scapuloperoneal syndrome and oculocraniosomatic syndrome.
Observational (n=892)
A small subset of patients with chronic heart block have associated neuromuscular diseases, highlighting the importance of recognizing systemic or neurological conditions in these patients.
Rare neuromuscular associations in chronic heart block merit clinical consideration; cross-sectional data leave screening value and prevalence open.
A large group of patients with chronic heart block was studied for evidence of neurological disorder. Six out of 892 patients were found who had neuromuscular disease related to the conduction disturbance. In four patients, cardiac involvement appeared selectively to affect the conducting tissues. Three of these patients had a scapuloperoneal syndrome, the fourth, the oculocraniosomatic syndrome. In the remaining two patients, one with limb girdle dystrophy and the other with dystrophia myotonica, cardiomyopathy was present in addition to the conduction disturbance.
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Lambert et al. (1976) conducted an observational in Chronic heart block (n=892). Chronic heart block was evaluated on Neuromuscular disease related to the conduction disturbance. Among 892 patients with chronic heart block, 6 (0.67%) had neuromuscular disease related to the conduction disturbance, including scapuloperoneal syndrome and oculocraniosomatic syndrome.
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