Key result
Aortic surgery with a pantaloon graft in a 41-year-old man with severe supravalvular aortic stenosis reduced the mean gradient across the aorta from 48 to 8 mmHg.
Why the study?
Does aortic surgery with a pantaloon graft improve hemodynamics in an adult with isolated diffuse supravalvular aortic stenosis?
Case Report (n=1)
Does aortic surgery with a pantaloon graft improve hemodynamics in an adult with isolated diffuse supravalvular aortic stenosis?
Absolute Event Rate: 8% vs 48%
Aortic surgery with a pantaloon graft successfully treated severe isolated diffuse supravalvular aortic stenosis in an adult, significantly reducing the transaortic gradient.
Pantaloon graft may be feasible for adult supravalvular aortic stenosis; leaves open need for prospective validation.
Isolated supravalvular aortic stenosis in adults is a rare form of left ventricular outflow tract obstruction. We describe a case in a 41-year-old man in whom the supravalvular aorta had narrowed to approximately the size of the left anterior descending coronary artery. The patient underwent aortic surgery with replacement of the ascending aorta and repair of supravalvular aortic stenosis with a pantaloon graft. A postoperative echocardiogram showed substantial improvement: the mean gradient across the aorta had fallen from 48 to 8 mmHg. Surgery is the definitive treatment in symptomatic patients with supravalvular aortic stenosis.
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Namana et al. (2017) conducted a case report in Isolated diffuse supravalvular aortic stenosis (n=1). Aortic surgery with replacement of the ascending aorta and repair of supravalvular aortic stenosis with a pantaloon graft was evaluated on Mean gradient across the aorta. Aortic surgery with a pantaloon graft in a 41-year-old man with severe supravalvular aortic stenosis reduced the mean gradient across the aorta from 48 to 8 mmHg.
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