Key result
Radiofrequency ablation successfully cured concomitant atrioventricular reentrant tachycardia and typical atrioventricular nodal tachycardia in a patient with Williams syndrome.
Case Report (n=1)
This case report describes the first known instance of concomitant AVRT and AVNRT in a patient with Williams syndrome, which was successfully treated with radiofrequency ablation.
Ablation may be feasible for dual AVRT/AVNRT in Williams syndrome; leaves open generalizability beyond this single case.
Williams syndrome is characterized by a constellation of features including mental retardation and supravalvular aortic stenosis. Other cardiovascular abnormalities including arrhythmias contributing to sudden death have been described in these patients. In this report we describe a case of a 49-year-old female with Williams syndrome who presented with severe symptomatic supraventricular tachycardia. Cardiac electrophysiology study identified a left posteroseptal concealed accessory bypass tract responsible for atrioventricular reentrant tachycardia and a concomitant typical atrioventricular nodal tachycardia. Such unusual association of combination of two different types of supraventricular tachycardia and Williams syndrome has not been previously reported. Radiofrequency ablation was successfully performed to cure these arrhythmias.
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Kantharia et al. (1999) conducted a case report in Williams syndrome with severe symptomatic supraventricular tachycardia (n=1). Radiofrequency ablation was evaluated on Cure of arrhythmias. Radiofrequency ablation successfully cured concomitant atrioventricular reentrant tachycardia and typical atrioventricular nodal tachycardia in a patient with Williams syndrome.
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