Key result
Dermatofibrosarcoma protuberans is a rare soft tissue tumour with characteristic histologic features and imaging findings that should prompt its inclusion in differential diagnoses.
MRI features, while not pathognomonic, combined with characteristic location and shape can aid in the differential diagnosis of Dermatofibrosarcoma protuberans.
Supports considering DFSP in differentials for characteristic lesions; leaves open prospective validation of imaging criteria.
Dermatofibrosarcoma protuberans (DFSP) is a rare slow-growing soft tissue tumour which characteristically occurs on the chest, head and neck regions. Typical histologic features include monomorphous spindle-shaped cells arranged in a storiform pattern on a background of fibrous stroma. The tumour has a propensity for local invasion and high recurrence rate. While the imaging features are not pathognomonic of the tumour, the characteristic location and shape should prompt inclusion in the differential diagnostic list.
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Bergin et al. (2007) conducted a review in Dermatofibrosarcoma protuberans (DFSP). Dermatofibrosarcoma protuberans is a rare soft tissue tumour with characteristic histologic features and imaging findings that should prompt its inclusion in differential diagnoses.
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