Key result
Careful anesthetic management is necessary and was described for a two-months-old male child with Walker-Warburg Syndrome undergoing an elective ventriculo-peritoneal shunt operation.
Case Report (n=1)
Highlights the necessity of careful anesthetic management in children with Walker-Warburg syndrome due to complex multisystem involvement.
May inform anesthetic strategies for Walker-Warburg syndrome; leaves open broader evidence on optimal management.
BACKGROUND AND OBJECTIVES: Walker-Warburg Syndrome is a rare, autosomal recessive congenital muscular dystrophy manifested by central nervous system, eye malformations and possible multisystem involvement. The diagnosis is established by the presence of four criteria: congenital muscular dystrophy, type II lissencephaly, cerebellar malformation, and retinal malformation. Most of the syndromic children die in the first three years of life because of respiratory failure, pneumonia, seizures, hyperthermia and ventricular fibrillation. CASE REPORT: The anesthetic management of a two-months-old male child listed for elective ventriculo-peritoneal shunt operation was discussed. CONCLUSIONS: A careful anesthetic management is necessary due to the multisystem involvement. We reported anesthetic management of a two-months-old male child with Walker-Warburg Syndrome who was listed for elective ventriculo-peritoneal shunt operation.
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Köse et al. (2013) conducted a case report in Walker-Warburg Syndrome (n=1). Anesthetic management was evaluated. Careful anesthetic management is necessary and was described for a two-months-old male child with Walker-Warburg Syndrome undergoing an elective ventriculo-peritoneal shunt operation.
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