Pulmonary Arterial Hypertension Management – A New Approach For a Rare Disease

Pulmonary Arterial Hypertension is a rare, deadly and incurable condition for which management guidelines have recently been revised. Important and remarkable changes include a new strategy-oriented treatment algorithm, based on a risk-stratification approach. Combination therapy is recommended as soon as diagnosis is established for all patients, with a parenteral prostacyclin for the most severe cases. The uncommon nature of the disease and the management complexity require that care is delivered by expert specialised centers.