Key result
β-thalassemia is associated with high rates of pulmonary hypertension, developing in 10% of patients with thalassemia major and over 50% of those with thalassemia intermedia.
Case report on the use of long-term oral sildenafil for pulmonary hypertension in a patient with thalassemia.
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Alerts clinicians to screen thalassemia patients for PH; case-report data leave sildenafil role open for prospective trials.
Littera et al. (2002) studied this question. β-thalassemia is associated with high rates of pulmonary hypertension, developing in 10% of patients with thalassemia major and over 50% of those with thalassemia intermedia.
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