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Arterial tourniquet use in an infant with Timothy syndrome triggered life-threatening arrhythmias, likely secondary to excess sympathetic stimulation.
Arterial tourniquets may trigger life-threatening arrhythmias in patients with Timothy syndrome due to excess sympathetic stimulation.
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Tourniquets warrant caution in Timothy syndrome; single case leaves open generalizability and preventive strategies.
An infant with Timothy syndrome, a congenital syndrome resulting in a long QT interval and high risk of death in childhood, is presented along with his perioperative management. Characteristic life-threatening arrhythmias thought to be caused by excess sympathetic stimulation secondary to an arterial tourniquet are described.
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Yates et al. (2007) studied this question. Arterial tourniquet use in an infant with Timothy syndrome triggered life-threatening arrhythmias, likely secondary to excess sympathetic stimulation.
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