Progression of the EEG in Lafora-Body Disease

.Lafora-body disease is classified as progressive myoclonus epilepsy. The disease is characterized by the triad of epilepsy, myoclonus, and progressive dementia. Deposits called Lafora bodies are found in the central nervous system and other organs, including the liver and skin. In this case history, the diagnosis of Lafora-body disease was confirmed by the finding of Lafora bodies in a skin biopsy. The EEG in Lafora's disease has consistently been reported as abnormal. As the patient deteriorates clinically, the EEG also deteriorates, as shown in our case study.