Why the study?
While the role of dystroglycan signaling is well established in inherited disorders such as Duchenne muscular dystrophy, it is less studied in acquired HFrEF.
Design
Review
Key result
Dystroglycan signaling, essential for sarcolemma stability, is emerging as a key factor in cardiac remodeling and fibrosis in acquired heart failure with reduced ejection fraction.
Authors
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Dystroglycan modulation should not yet inform HFrEF care; extends its role from inherited dystrophies but remains hypothesis-generating.
Dystroglycan remodeling may play a significant role in the pathophysiology of acquired HFrEF, extending its known importance beyond inherited muscular dystrophies.
Pradhan et al. (2026) conducted a review in Heart failure with reduced ejection fraction (HFrEF). Dystroglycan signaling was evaluated. Dystroglycan signaling, essential for sarcolemma stability, is emerging as a key factor in cardiac remodeling and fibrosis in acquired heart failure with reduced ejection fraction.