Key result
Surgical resection of a primary cardiac intimal sarcoma presenting as functional mitral stenosis was successfully performed with negative margins.
Case Report (n=1)
Primary cardiac intimal sarcoma is a rare and aggressive tumor that can present as functional mitral stenosis and heart failure, requiring early diagnosis and surgical resection for improved survival.
May support surgical resection in rare cardiac intimal sarcoma; leaves open need for prospective outcome data.
Cardiac intimal sarcomas are extremely rare, remarkably aggressive and least reported type of primary malignant tumors of the heart. Cardiac intimal sarcomas are encountered more commonly in the large arterial blood vessels including pulmonary artery and aorta, and are extremely rare in the heart. The mainstay of treatment is achievement of tumor-free margins with surgical resection, which is associated with improved survival. Here, we report a 66-year-old female with primary cardiac intimal sarcoma presented with functional mitral stenosis and heart failure. This case report emphasizes common presentation of a rare disease, and the significance of early diagnosis and timely intervention.
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Vinod et al. (2018) conducted a case report in Primary cardiac intimal sarcoma (n=1). Surgical resection was evaluated. Surgical resection of a primary cardiac intimal sarcoma presenting as functional mitral stenosis was successfully performed with negative margins.
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