Why the study?
Sporadic inclusion body myositis is an intractable, progressive muscle disease of unknown etiology without effective treatment, and its cross-sectional profile in Japan needed elucidation.
Population
146 patients diagnosed with sIBM across Japan
Design
Multicenter cross-sectional questionnaire survey
Key result
In a cross-sectional survey of Japanese patients with sporadic inclusion body myositis, the mean time from onset to diagnosis was 55.5 months, with 73% of patients reporting psychological anxiety.
Authors
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Diagnostic delays and burdens in sporadic inclusion body myositis merit clinical vigilance; leaves open optimal strategies for earlier recognition in rare myopathies.
Cross-Sectional (n=146)
Yes
Patients with sporadic inclusion body myositis in Japan experience significant diagnostic delays and high rates of psychological and financial anxiety.
Suzuki et al. (2016) conducted a cross-sectional in Sporadic inclusion body myositis (sIBM) (n=146). Sporadic inclusion body myositis (sIBM) was evaluated on Cross-sectional clinical profile, diagnostic delay, and patient-reported anxiety. In a cross-sectional survey of Japanese patients with sporadic inclusion body myositis, the mean time from onset to diagnosis was 55.5 months, with 73% of patients reporting psychological anxiety.
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