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October 28, 2024The International Journal of Cardiovascular ImagingOpen Access

Intramyocardial fatty infiltration lesion in sporadic inclusion body myositis: a case report

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Key result

CMR identifies intramyocardial fatty infiltration in a patient with sporadic inclusion body myositis.

  • n=1

Why the study?

Cardiac involvement in sporadic inclusion body myositis is rare and its exact frequency remains unclear, prompting this case description and literature analysis.

Population

A 73-year-old woman diagnosed with sporadic inclusion body myositis

Design

Case report

Authors

BRBetim RedzepiMTMarie ThéaudinSBSamir Bengueddache

Discussion

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Overview

Raises possibility of cardiac involvement in sporadic inclusion body myositis; hypothesis-generating and requires confirmation before clinical consideration.

Study Design

Type

Case Report (n=1)

Multicenter

No

Structured PICO

P
Population
A 73-year-old woman with sporadic inclusion body myositis who was found to have intramyocardial fatty infiltration on cardiac magnetic resonance imaging.
I
Intervention
Cardiac magnetic resonance (CMR) imaging
O
Outcome
Detection of intramyocardial lesionssurrogate

CMR can detect subtle cardiac manifestations such as intramyocardial fatty infiltration in patients with sporadic inclusion body myositis, potentially offering prognostic value.

Limitations

  • Single case report
  • No cardiac biopsy performed to histologically confirm the lesions
  • Lack of large cohort studies to establish the frequency of these findings

Cite This Study

Redzepi et al. (2024) conducted a case report in Sporadic inclusion body myositis (sIBM) (n=1). Cardiac magnetic resonance (CMR) was evaluated on Detection of intramyocardial lesions. Cardiac magnetic resonance imaging identified intramyocardial lesions consistent with fatty infiltration in a patient with sporadic inclusion body myositis.

synapsesocial.com/papers/6a5e2263dec751667c70adc7https://doi.org/10.1007/s10554-024-03271-z
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Also Consider

Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context:

  1. 1The heart in sporadic inclusion body myositis: a study in 51 patients2009 · 54 citations
  2. 2[Sporadic Inclusion Body Myositis].2024
  3. 3Sporadic inclusion body myositis: overreliance on histology may lead to misdiagnosis2026
  4. 4Quantitative muscle MRI in sporadic inclusion body myositis (sIBM): A prospective cohort study2024 · 4 citations
  5. 5Mitochondrial defects in sporadic inclusion body myositis—causes and consequences2024