Key result
Bentall procedure recommended for a 25-year-old Marfan syndrome patient with a giant aortic root aneurysm.
Why the study?
Marfan's syndrome patients have a predisposition for progressive aortic root and ascending aortic dilation requiring periodic monitoring and timely intervention.
Case Report (n=1)
Highlights the presentation of a giant aortic root aneurysm in a young man with Marfan's syndrome, emphasizing the need for periodic echocardiographic monitoring.
Answers are grounded in this paper and cite their sources.
Highlights aortic complications in symptomatic young Marfan patients; leaves open optimal intervention thresholds.
A 25-year-old man came to our clinic with the complaints of exertional palpitations and dyspnea. He had skeletal features suggestive of Marfan's syndrome. Contrast-enhanced computed tomography confirmed aneurysmal dilation of the aortic root and the proximal part of the ascending aorta. The patient was advised to undergo Bentall procedure for replacement of the aortic valve, aortic root, and ascending aorta. Marfan's syndrome is a connective tissue disorder with autosomal-dominant inheritance. Patients have a predisposition for progressive aortic root and ascending aortic dilation, and should undergo periodic echocardiographic monitoring.
No takes yet. Share an insight, caveat, or question.
Bhasin et al. (2021) conducted a case report in Marfan's syndrome with giant aortic root aneurysm (n=1). Bentall procedure was evaluated. A 25-year-old man with Marfan's syndrome presented with a giant aortic root aneurysm and was advised to undergo the Bentall procedure for aortic replacement.
Synapse has enriched 10 related papers. Consider them for comparative context: