Highlights the critical need for lifelong imaging follow-up in patients with Marfan's syndrome after supracoronary aortic repair due to the high risk of developing giant aortic root aneurysms.
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May warrant ongoing aortic surveillance after repair in Marfan syndrome; leaves open optimal long-term protocols.
The risk of aortic dissection and aortic aneurysm in patients with Marfan syndrome has been known for years. A 46-year-old man with Marfan?s syndrome was admitted to our clinic with a complaint of chest pain and palpitation in the last year. Hemiarcus replacement, aortic valve resuspension and graft interposition between innominate artery and prosthetic ascending aorta was performed 4 years ago due to type 1 aortic dissection. Echocardiography and computed tomography revealed dilatation of aortic root (68 mm in diameter), with advanced aortic valve insufficiency. Hence, we successfully performed aortic root replacement with Bentall procedure. The postsurgical course was uneventful. We conclude that aortic root aneurysm is a significant long-term complication after repair of the ascending aorta in patients with Marfan?s syndrome, and these patients should be follow-up close and lifelong in terms of development of aneurysm at the level of the residual aorta.
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Arslan et al. (2018) studied this question.
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