Key result
CMR identifies isolated LV apical hypoplasia featuring a truncated spherical LV and apical fat.
Why the study?
Isolated left ventricular apical hypoplasia is a rare, unclassified cardiomyopathy with typical imaging findings that require detailed characterization.
Case Report (n=1)
No
Cardiac magnetic resonance is a valuable multimodal imaging tool for identifying the characteristic structural anomalies of the rare cardiomyopathy isolated left ventricular apical hypoplasia.
Isolated left ventricular apical hypoplasia (ILVAH) is a rare, unclassified cardiomyopathy with typical imaging findings. Cardiac magnetic resonance (CMR) is valuable for identifying heart structural anomalies. This case report describes the detection of significant anatomical abnormalities in the left ventricle (LV) with CMR in a 32-year-old man who presented with sudden dyspnea at authors' institution. This case demonstrates the characteristics of ILVAH under multimodal imaging: A truncated spherical shape of the LV, encircling of the distal LV by the right ventricle, the presence of fat replacement at the apex, and without abnormality in the mitral valve or aorta.
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Hu et al. (2025) conducted a case report in Isolated left ventricular apical hypoplasia (n=1). Cardiac magnetic resonance (CMR) was evaluated on Detection of anatomical abnormalities. Cardiac magnetic resonance identified isolated left ventricular apical hypoplasia characterized by a truncated spherical left ventricle, distal encircling by the right ventricle, and apical fat.
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