Key result
Approximately 10% of patients diagnosed with pulmonary arterial hypertension without a demonstrable cause have a family history of the disease (familial PAH).
Provides an overview of the classification of pulmonary hypertension, highlighting that approximately 10% of PAH cases without a demonstrable cause are familial.
ulmonary hypertension can be classified into 4 categories: pulmonary arterial hypertension (PAH), pulmonary venous hypertension, pulmonary hypertension associated with hypoxemia, and pulmonary hypertension due to chronic thrombotic or embolic disease.PAH is a progressive and often fatal condition that predominantly affects women.Approximately 10% of patients diagnosed with PAH without a demonstrable cause have a family history of the disease and are referred to as having familial PAH (FPAH), whereas the remainder are classified as having idiopathic PAH (IPAH).
No takes yet. Share an insight, caveat, or question.
Yuan et al. (2005) conducted a review in Pulmonary Arterial Hypertension. Approximately 10% of patients diagnosed with pulmonary arterial hypertension without a demonstrable cause have a family history of the disease (familial PAH).
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: