Key result
Primary pulmonary Extraskeletal Ewing Sarcoma manifests as a large lung mass extending to the LA.
Why the study?
Extraskeletal Ewing Sarcoma is rarely reported, especially presenting as a large lung mass in adolescents.
Case Report (n=1)
No
Extraskeletal Ewing Sarcoma can rarely present as a large lung mass extending into the left atrium via the pulmonary vein.
May warrant inclusion of extraskeletal Ewing sarcoma in differentials for pediatric lung masses with atrial extension; leaves open need for multicenter registries.
Extraskeletal Ewing Sarcoma is rarely reported. A fifteen-year-old girl presented with the right-sided pleuritic chest pain, shortness of breath, and productive cough with whitish sputum associated with poor oral intake. She subsequently underwent contrast-enhanced Computerized Tomography thorax, which showed lobulated heterogenous hypodensity occupying the entrance of the right superior pulmonary vein, extending to the left atrium.
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Pyn et al. (2023) conducted a case report in Primary pulmonary Extraskeletal Ewing Sarcoma (n=1). Right pneumonectomy and evacuation of left atrium mass was evaluated. A 15-year-old girl presenting with a large lung mass extending to the left atrium was diagnosed with primary pulmonary Extraskeletal Ewing Sarcoma, highlighting this rare diagnosis in young patients.
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