Key result
Surgical resection followed by 3 cycles of chemotherapy resulted in clinical stability with no signs of recurrence or hydrothorax in a 15-year-old girl with primary pulmonary Ewing's sarcoma.
Why the study?
Primary pulmonary Ewing's sarcoma is an extremely rare malignancy that can present in visceral organs.
Case Report (n=1)
Primary pulmonary Ewing's sarcoma is a rare cause of massive hemothorax that can be successfully treated with emergency surgery and chemotherapy.
Consider primary pulmonary Ewing sarcoma in adolescents with massive hemothorax; extends rare extra-skeletal spectrum but remains hypothesis-generating.
BACKGROUND: Ewing's sarcoma is a common malignant bone tumor in children and young adults. Rarely, extra-skeletal soft tissues and visceral organs can also be the site of origin of Ewing's sarcoma. Primary pulmonary Ewing's sarcoma is an extremely rare malignancy. CASE PRESENTATION: We report an unusual case of primary pulmonary Ewing's sarcoma in a 15-year-old girl who initially presented with massive hemothorax. By histopathology evaluation of surgical biopsy specimens, the diagnosis of extraosseous Ewing's sarcoma was confirmed by both light microscopy and immunohistochemistry. Emergency, open surgery was performed by thoracic surgery at an early stage. After 3 cycles of chemotherapy, the patient was found to be stable at follow-up examination. No more hydrothorax or other symptoms. CONCLUSIONS: We have described an extremely rare case of primary pulmonary Ewing's sarcoma with massive hemothorax. The patient underwent surgical resection and postoperative chemotherapy, no sign of recurrence to date as an outcome.
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Ling et al. (2021) conducted a case report in Primary pulmonary Ewing's sarcoma with massive hemothorax (n=1). Surgical resection and postoperative chemotherapy was evaluated on Clinical outcome (recurrence and symptoms). Surgical resection followed by 3 cycles of chemotherapy resulted in clinical stability with no signs of recurrence or hydrothorax in a 15-year-old girl with primary pulmonary Ewing's sarcoma.
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