The Performance of Upper Limb (PUL) module in limb-girdle muscular dystrophy.

Figures

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  Figure 1.. Box-and-whisker plot representing the median (white line within the box), the interquartile range (length of the box), the 90th and the 10th percentiles (whiskers above and below the box) of the item K (top left, i.e.: stacking light cans), N (top middle, i.e.: Tearing paper) and R (top right, i.e.: Picking up coins) of the PUL score measured on LGMD2A/R1 (R1/2A, red) and LGMD2B/R2 (R2/2B, blue) patients. Box-and-whisker plot representing the median (white line within the box), the interquartile range (length of the box), the 90th and the 10th percentiles (whiskers above and below the box) of the mean MRC score of all the muscles involved in item K (bottom left, i.e.: Biceps brachialis, triceps brachialis, wrist extensor and flexor, opponent of the thumb and hand grip muscles), N (bottom middle, i.e.: Biceps brachialis, triceps brachialis, wrist extensor and flexor, opponent of the thumb and hand grip muscles) and R (bottom right, i.e.: Wrist extensor, opponent of the thumb, interosseous and hand prehension muscles) of the PUL score measured on LGMD2A/R1 (R1/2A, red) and LGMD2B/R2 (R2/2B, blue) patients. The p-values are also reported in white.

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  Figure 2.. Scatter plot of the mean muscles MRC score (x-axis) and the corresponding function (y-axis) measured on LGMD2A/R1 (R1/2A, red) and LGMD2B/R2 (R2/2B, blue) patients. The mean muscles MRC score for item K (left, i.e.: stacking light cans) was computed by calculating the average of the MRC score of the trapezius, the deltoids and the biceps brachialis muscles. The mean muscles MRC score for item N (middle, i.e.: Tearing paper), was computed by calculating the average of the MRC score of the biceps brachialis, the triceps brachialis, the wrist extensor and flexor, the opponent of the thumb and the hand grip muscles. The mean muscles MRC score for item R (right, i.e.: Picking up coins) was computed by calculating the average of the MRC score of the wrist extensor, the opponent pollicis, the interosseous and the hand prehension muscles were pooled. The intercept and the slope of the linear regression lines (short-dashed lines) as well as the coefficient of determination (r2) are also shown. The vertical dash-dotted green lines indicate the threshold when muscle contracts and moves with no resistance.