Malignant solitary fibrous tumour of the orbit

PURPOSE: We aimed to report a case of orbital solitary fibrous tumour (SFT) in a child and to review the relevant literature. METHODS: We describe an SFT in a 13-year-old boy with a 1-month history of painless proptosis in the left eye. RESULTS: Magnetic resonance imaging revealed a well circumscribed mass filling most of the left intraconal orbit. The lesion was excised and histopathological examination revealed a malignant SFT. Postoperative follow-up for 18 months was uneventful. CONCLUSIONS: Malignant SFT of the orbit should be included in the differential diagnosis of paediatric orbital tumours. Complete surgical excision remains the preferred method of management and the longterm prognosis is guarded.