Nephrotic syndrome associated with DICER1-associated primary intracranial sarcoma

This is the authors' abstract. We don't add key points for this paper.

A 14-year-old female presented with a one-month history of headache and dizziness accompanied by acute vomiting. She had previously been diagnosed with nephrotic syndrome. Brain MRI demonstrated a large, well-defined solid mass in the left frontal lobe with prominent flow-void vessels (Fig. 1A, arrow) and minimal hemorrhage (Fig. 1B, arrowhead), which showed marked contrast enhancement (Fig. 1C). The patient subsequently underwent neuronavigation-guided surgical resection.