Key result
Surgical correction, including aortic and mitral membrane excision and aortic root enlargement, was successfully performed in a patient with Shone complex and a persistent left superior vena cava.
Why the study?
Shone complex is a rare congenital cardiac anomaly typically observed in children, with limited reports of adult presentations and associated venous anomalies.
Case Report (n=1)
Successful repair shows technical feasibility in Shone complex with PLSVC; larger studies needed before broader adoption.
Parachute mitral valve complex is an unusual congenital anomaly described by Shone et al. It is characterized by a parachute deformity of the mitral valve associated with additional forms of left heart anomalies, such as aortic valvular stenosis and coarctation of the aorta. Fewer than 50 cases of Shone's complex have been reported in the literature, and it has only been observed in children. We report the case of a 33-year-old man who was referred to our department because of atrial fibrillation. Echocardiographic evaluation and aortogram evidenced a Shone's complex, including a parachute mitral valve anomaly, an aortic bicuspid valvular anomaly, and a coarctation of the aorta.
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Prunier et al. (2001) conducted a case report in Shone's complex (n=1). Surgical correction was evaluated. Surgical correction, including aortic and mitral membrane excision and aortic root enlargement, was successfully performed in a patient with Shone complex and a persistent left superior vena cava.
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