Paroxysmal Nocturnal Hemoglobinuria with a Common Variable Immunodeficiency Phenotype: Noncirrhotic Portal Hypertension Without Demonstrable Splanchnic Thrombosis

thrombotic mechanism, and new cytopenias should prompt evaluation for hypersplenism before assuming marrow failure [1].Whether the co-occurrence with CVID is coincidental remains unclear, but the practical message stands: in PNH, a patent macrovasculature does not equate to the absence of thrombosis.