Claustrum Sign in Hashimoto Encephalopathy Presenting With New Onset Refractory Status Epilepticus ( NORSE ): First Report of a Rare Phenotype

Key Points

• To investigate the significance of the claustrum sign in diagnosing Hashimoto's encephalopathy presenting with NORSE.
• Case report detailing the presentation and diagnosis of a patient with NORSE and the claustrum sign.
• Clinical assessment including imaging and treatment response analysis.
• Identification of the bilateral claustrum sign in a patient with new-onset refractory status epilepticus.
• Successful treatment with corticosteroids, leading to clinical improvement.