Case report reveals enlarged endolymphatic sac causing sensorineural hearing loss in a child, suggesting rare pathology.
This is the case of a healthy 10-year-old girl presenting to the pediatric otolaryngology clinic for an incidental finding of a 20 mm dilatation within the left posterior fossa on brain computed tomography done for evaluation of left retro-auricular pain. Comprehensive audiometry showed left sensorineural hearing loss at low frequencies. Magnetic resonance imaging revealed a cystic lesion along the posterior aspect of the left temporal bone with normal inner ear anatomy consistent with an enlarged endolymphatic sac anomaly. This pathology is a rare entity with only one previously reported case in the literature.
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Daou et al. (2025) studied this question.
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