A Rare Cardiac Malformation: Isolated Double‐Orifice Mitral Valve

The double‐orifice mitral valve (DOMV) is a rare congenital valve malformation characterized by a mitral valve with a single fibrous annulus, resulting in two orifices. Due to a lack of understanding and awareness of its echocardiographic or coronary computed tomographic angiography (CCTA) characteristics, there is a risk of misdiagnosis. We report a case of a 64‐year‐old woman who was found to have an isolated double orifice mitral valve malformation on transthoracic echocardiography and CCTA. Echocardiography is the first‐line tool for diagnosing DOMV. CCTA is critical in the complementary diagnosis of DOMV combined with other coronary artery anomalies and extracardiac structure abnormalities.