This case report highlights the utility of multimodality imaging (TTE, TEE, and CMR) in diagnosing a rare incomplete form of Shone's complex involving a double-orifice mitral valve and bicuspid aortic valve.
Multimodality imaging may aid diagnosis of rare incomplete Shone variants; leaves open prevalence, outcomes, and management data.
Double-orifice mitral valve (DOMV) is a rare congenital malformation characterized by two separate valve orifices of varying sizes in association with the abnormalities of the subvalvular apparatus. It has been reported to be associated with a variety of other congenital malformations. We report a rare case of incomplete form of Shone's complex composed of a complete bridge-type DOMV and bicuspid aortic valve, well demonstrated by both transthoracic and transoesophageal echocardiography and cardiac magnetic resonance imaging.
No takes yet. Share an insight, caveat, or question.
Erkol et al. (2009) studied this question.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: