Anesthetic Management of Pediatric Splenectomy With Thalassemia Major and Evans Syndrome : A Case Report

In Beta-thalassemia major disease, patient need multiple blood products which are regular and frequent which ultimately leads to autoimmunization reactions . In our case of an 8 year old male child , who received frequent blood transfusion because of Beta-thalassemia, diagnosed with Evans syndrome ; posted for Splenectomy. As Evans syndrome leads to autoimmune pancytopenia. Here we report such case in view to increase awareness about disease and prevent it by regular screening and prenatal diagnostic modalities.