Typical Electrocardiographic Features in Arrhythmogenic Left Ventricular Cardiomyopathy

Since 2020 arrhythmogenic cardiomyopathy includes a right dominant form, a biventricular form and a left dominant form. Already in 2004 Carvajal syndrome was first described in Ecuador within families [1]. This syndrome includes a slighty dilated, poor contracting left ventricle and hair and skin abnormalities with curly hair and plantopalmar keratosis. The genetic background were mutations of the desmoplakin gene.