Adult-onset inflammatory linear verrucous epidermal nevus successfully treated with intralesional steroid

Inflammatory linear verrucous epidermal nevus (ILVEN) is a rare dermatosis presenting as pruritic, hyperkeratotic, and erythematous papules and plaques arranged along the lines of Blaschko. Histologically, it is characterized by epidermal acanthosis with alternating para- and orthokeratosis and a perivascular lymphocytic infiltrate.1 It usually appears in children,2 with only 19 adult cases reported in literature.1 ILVEN harbors features of both a hamartoma and an inflammatory disorder. Initial descriptions of its early onset, histology, and recalcitrance to therapy helped classify it as a type of epidermal nevus.