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March 24, 2026European Respiratory Journal

Primary ciliary dyskinesia: Respiratory tract infections and impact of pseudomonas aeruginosa

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Authors

SLSylvaine LefeuvreEDEric DeneuvilleJDJacques Deblic

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Overview

Retrospective multicenter study identifies bacterial infections in primary ciliary dyskinesia and implications for lung function.

Key Points

  • This study aims to identify bacteria causing respiratory infections in children with primary ciliary dyskinesia and evaluate lung function outcomes after colonization.
  • Retrospective multicenter study design
  • Assessment of microbiological sputum from patients with PCD
  • Evaluation of lung function decline associated with Pseudomonas aeruginosa infection
  • Identification of risk factors for Pseudomonas aeruginosa acquisition
  • Identified five main bacteria in sputum samples: Haemophilus influenzae (64.8%), Streptococcus pneumoniae (48.6%), Pseudomonas aeruginosa (27.7%), Staphylococcus aureus (17.1%), and Moraxella catarrhalis (16.2%)
  • Pseudomonas aeruginosa infection linked to a significant decline in Forced Expiratory Volume in one second (FEV1) values (p = 0.01)
  • Only age emerged as a risk factor for Pseudomonas aeruginosa infection
  • No clinical degradation observed with other pathogens, maintaining stable FEV1

Cite This Study

Lefeuvre et al. (2014) studied this question.

synapsesocial.com/papers/69c229b2aeb5a845df0d47cahttps://doi.org/10.1183/13993003/erj.44.suppl_58.p1153
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Also Consider

Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context:

  1. 1C61-05 Airway Microbiologic Profile in Primary Ciliary Dyskinesia: A Single-center Study2026
  2. 2Respiratory bacterial epidemiology at three primary ciliary dyskinesia clinical centers2026 · 2 citations
  3. 3Associations between respiratory pathogens and lung function in primary ciliary dyskinesia: cross-sectional analysis from the PROVALF-PCD cohort2024 · 18 citations
  4. 4Primary Ciliary Dyskinesia: Insights from a Portuguese tertiary centre cohort2026
  5. 5D105-12 Prevalence and Age-related Acquisition of Airway Pathogens in Pediatric Primary Ciliary Dyskinesia2026