January 4, 2017New England Journal of Medicine711 citations
View Full PaperArrhythmogenic Right Ventricular Cardiomyopathy
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Abstract
Arrhythmogenic right ventricular cardiomyopathy is a heritable heart-muscle disorder that causes progressive replacement of right ventricular myocardium by fibrofatty tissue. Mutations in genes encoding desmosomal proteins play a key role in the pathogenesis of the disease.